Generalized idiopathic epilepsy and epileptic syndromes not intractable without status epilepticus

MDC 01 Diseases & Disorders of the Nervous System Seizures

G40001 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, with status epilepticus G40009 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, without status epilepticus G40011 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, with status epilepticus G40019 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, without status epilepticus G40101 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, with status epilepticus G40109 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, without status epilepticus G40111 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, with status epilepticus G40119 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, without status epilepticus G40201 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, with status epilepticus G40209 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, without status epilepticus G40211 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, with status epilepticus G40219 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, without status epilepticus G40301 Generalized idiopathic epilepsy and epileptic syndromes, not intractable, with status epilepticus G40309 Generalized idiopathic epilepsy and epileptic syndromes, not intractable, without status epilepticus G40311 Generalized idiopathic epilepsy and epileptic syndromes, intractable, with status epilepticus G40319 Generalized idiopathic epilepsy and epileptic syndromes, intractable, without status epilepticus G40401 Other generalized epilepsy and epileptic syndromes, not intractable, with status epilepticus G40409 Other generalized epilepsy and epileptic syndromes, not intractable, without status epilepticus G40411 Other generalized epilepsy and epileptic syndromes, intractable, with status epilepticus G40419 Other generalized epilepsy and epileptic syndromes, intractable, without status epilepticus G40501 Epileptic seizures related to external causes, not intractable, with status epilepticus G40509 Epileptic seizures related to external causes, not intractable, without status epilepticus G40801 Other epilepsy, not intractable, with status epilepticus G40802 Other epilepsy, not intractable, without status epilepticus G40803 Other epilepsy, intractable, with status epilepticus G40804 Other epilepsy, intractable, without status epilepticus G40811 Lennox-Gastaut syndrome, not intractable, with status epilepticus G40812 Lennox-Gastaut syndrome, not intractable, without status epilepticus G40813 Lennox-Gastaut syndrome, intractable, with status epilepticus G40814 Lennox-Gastaut syndrome, intractable, without status epilepticus G40821 Epileptic spasms, not intractable, with status epilepticus G40822 Epileptic spasms, not intractable, without status epilepticus G40823 Epileptic spasms, intractable, with status epilepticus G40824 Epileptic spasms, intractable, without status epilepticus G4089 Other seizures G40901 Epilepsy, unspecified, not intractable, with status epilepticus G40909 Epilepsy, unspecified, not intractable, without status epilepticus G40911 Epilepsy, unspecified, intractable, with status epilepticus G40919 Epilepsy, unspecified, intractable, without status epilepticus G40A01 Absence epileptic syndrome, not intractable, with status epilepticus G40A09 Absence epileptic syndrome, not intractable, without status epilepticus G40A11 Absence epileptic syndrome, intractable, with status epilepticus G40A19 Absence epileptic syndrome, intractable, without status epilepticus G40B01 Juvenile myoclonic epilepsy, not intractable, with status epilepticus G40B09 Juvenile myoclonic epilepsy, not intractable, without status epilepticus G40B11 Juvenile myoclonic epilepsy, intractable, with status epilepticus G40B19 Juvenile myoclonic epilepsy, intractable, without status epilepticus R5600 Simple febrile convulsions R5601 Complex febrile convulsions R561 Post traumatic seizures R569 Unspecified convulsions

There are many different types of seizures.

New terms to describe and classify seizures have been developed by the International League Against Epilepsy. This was done to make the names of seizures more accurate, less confusing, and more descriptive of what is happening.

Listen to Drs. Joe Sirven and Bob Fisher discuss the changes in this episode of our  "Hallway Conversations" podcast series:

The new terms consider these important areas when describing seizures.

1. The onset or beginning of a seizure: Where seizures start in the brain tells a lot about what may occur during a seizure, what other conditions or symptoms may be seen, how they may affect someone and, most importantly, what treatment may be best for that seizure type. When we don’t know the onset of a seizure, the wrong treatment may be used. Or a person may not be offered a treatment that has the best chance of helping.
2. A person’s level of awareness during a seizure: Whether a person is aware or not tells a lot about the type of seizure. It’s also very important to know for a person’s safety.
3. Whether movements happen during a seizure: Seizures can also be described by whether motor symptoms occur. When no motor symptoms happen, it can be called a non-motor seizure. This level of description does not need to be used all the time, especially when generally describing or talking about seizures. Yet other times you may find the motor terms helpful.

How are seizures classified now?

There are now 3 major groups of seizures.

Generalized onset seizures:

These seizures affect both sides of the brain or groups of cells on both sides of the brain at the same time. This term was used before and still includes seizures types like tonic-clonic, absence, or atonic to name a few.

Focal onset seizures:

The term focal is used instead of partial to be more accurate when talking about where seizures begin. Focal seizures can start in one area or group of cells in one side of the brain.

• Focal Onset Aware Seizures: When a person is awake and aware during a seizure, it’s called a focal aware seizure. This used to be called a simple partial seizure.
• Focal Onset Impaired Awareness: When a person is confused or their awareness is affected in some way during a focal seizure, it’s called a focal impaired awareness seizure. This used to be called a complex partial seizure.

Unknown onset seizures:

When the beginning of a seizure is not known, it’s now called an unknown onset seizure. A seizure could also be called an unknown onset if it’s not witnessed or seen by anyone, for example when seizures happen at night or in a person who lives alone.

• As more information is learned, an unknown onset seizure may later be diagnosed as a focal or generalized seizure.

How are different symptoms during a seizure described?

Many different symptoms happen during a seizure. This new classification separates them simply into groups that involve movement.

For generalized onset seizures:

• Motor symptoms may include sustained rhythmical jerking movements (clonic), muscles becoming weak or limp (atonic), muscles becoming tense or rigid (tonic), brief muscle twitching (myoclonus), or epileptic spasms (body flexes and extends repeatedly).
• Non-motor symptoms are usually called absence seizures. These can be typical or atypical absence seizures (staring spells). Absence seizures can also have brief twitches (myoclonus) that can affect a specific part of the body or just the eyelids.

For focal onset seizures:

• Motor symptoms may also include jerking (clonic), muscles becoming limp or weak (atonic), tense or rigid muscles (tonic), brief muscle twitching (myoclonus), or epileptic spasms. There may also be automatisms or repeated automatic movements, like clapping or rubbing of hands, lipsmacking or chewing, or running.
• Non-motor symptoms: Examples of symptoms that don’t affect movement could be changes in sensation, emotions, thinking or cognition, autonomic functions (such as gastrointestinal sensations, waves of heat or cold, goosebumps, heart racing, etc.), or lack of movement (called behavior arrest).

For unknown onset seizures:

• Motor seizures are described as either tonic-clonic or epileptic spasms.
• Non-motor seizures usually include a behavior arrest. This means that movement stops – the person may just stare and not make any other movements.

What if I don’t know what type of seizures I or my loved one have?

How can I learn more?

• Read through the different seizures types listed in this section.
• Take information into your doctor or nurse along with a description of your seizures. Ask family or friends to write down what they see happening or to take a video. Then ask for help understanding your type of seizures.
• Find in-depth description of the seizure classification used by professionals and scientists here.

What is non intractable generalized idiopathic epilepsy?

What does without status epilepticus mean?

What is Epilepsy unspecified not intractable without status epilepticus?

What does it mean to have idiopathic epilepsy?